scleromyxedema syndrome with involvement of eyelids
نویسندگان
چکیده
purpose: to present a case of bilateral enlargement of eyelids in 29 year old man with sclromyxedema syndrome. case report: a 29- year- old man was referred to labbafinegad clinic with bilateral enlargment of upper and lower eyelids, and foreign body sensation since 9 year ago. investigating of patients history show renal deasese(hematuria ) since 9 year ago. in systemic examination the patients showed hands and feet involvement obviously. at further investhgations sclermyxderma was confirmed. conclusion: scleromyxedema is a rare, chronic and persistent idiopathic disorder characterized by a generalized papular eruption due to dermal mucin deposition with an increase in dermal collagen. uusually associated with a systemic involvement and paraproteinemia. the disease is characterized with mucin deposits in the skin and/or other organs. its etiology remains unknown affecting both genders equally between 30 and 50 years. the therapeutic options include numerous treatment modalities; however, no standard treatment exists as the rarity of this disease prevents the execution of controlled therapeutic trials.
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عنوان ژورنال:
بیناجلد ۲۱، شماره ۱، صفحات ۷۵-۷۸
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